{"id":47,"date":"2018-12-05T16:56:56","date_gmt":"2018-12-05T16:56:56","guid":{"rendered":"http:\/\/127.0.0.1:8080\/wordpress\/?page_id=47"},"modified":"2024-10-10T14:29:07","modified_gmt":"2024-10-10T12:29:07","slug":"cose-la-mastocitosi","status":"publish","type":"page","link":"https:\/\/www.asimas.it\/new_asimas\/cose-la-mastocitosi\/","title":{"rendered":"Cos&#8217;\u00e8 la mastocitosi?"},"content":{"rendered":"<div id=\"pl-47\"  class=\"panel-layout\" ><div id=\"pg-47-0\"  class=\"panel-grid panel-no-style\" ><div id=\"pgc-47-0-0\"  class=\"panel-grid-cell\" ><div id=\"panel-47-0-0-0\" class=\"so-panel widget widget_text panel-first-child panel-last-child\" data-index=\"0\" >\t\t\t<div class=\"textwidget\"><p align=\"left\"><span style=\"font-family: Georgia, Times New Roman, Times, serif; font-size: 20px; line-height: 30px;\"><br \/>\nLa mastocitosi \u00e8 una patologia rara, che include un gruppo di disordini estremamente eterogenei per sintomatologia, decorso clinico e prognosi, caratterizzati da proliferazione ed accumulo di mastociti patologici in differenti organi e tessuti.<\/span><\/p>\n<p align=\"left\"><span style=\"font-family: Georgia, Times New Roman, Times, serif; font-size: 20px; line-height: 30px;\"><br \/>\nGli organi prevalentemente interessati sono la cute e il midollo osseo; meno frequentemente possono essere coinvolti il fegato, la milza, il tratto gastrointestinale e i linfonodi. La proliferazione dei mastociti \u00e8 legata, nella maggior parte dei casi, a una mutazione somatica puntiforme del gene che codifica per KIT, il recettore del fattore delle cellule staminali (Stem Cell Factor, SCF).<\/span><\/p>\n<p align=\"left\"><span style=\"font-family: Georgia, Times New Roman, Times, serif; font-size: 20px; line-height: 30px;\"><br \/>\nSi definisce mastocitosi cutanea quando l\u2019accumulo di mastociti \u00e8 limitato alla cute e non si osservano alterazioni a carico di altri organi. La mastocitosi sistemica, al contrario, indica che esiste un coinvolgimento degli organi interni, indipendentemente dalla presenza o meno di lesioni cutanee.<\/span><\/p>\n<p align=\"left\"><span style=\"font-family: Georgia, Times New Roman, Times, serif; font-size: 20px; line-height: 30px;\"><br \/>\nI sintomi e i reperti clinici della mastocitosi possono dipendere dalla massiva liberazione di mediatori chimici contenuti in gran quantit\u00e0 nei mastociti, dall\u2019infiltrazione tissutale di mastociti e\/o dalla eventuale presenza di una neoplasia ematologica associata.<br \/>\n<\/span><\/p>\n<p align=\"left\">\n<p>&nbsp;<\/p>\n<p align=\"right\"><span style=\"font-family: Georgia, Times New Roman, Times, serif;\">A cura di Asimas &#8211; Associazione Italiana Mastocitosi<br \/>\nTesti a cura di RIMA &#8211; Rete Italiana Mastocitosi<br \/>\nDr.ssa Roberta Zanotti, Dr.ssa Patrizia Bonadonna,<br \/>\nProf. Massimo Triggiani<\/span><\/p>\n<\/div>\n\t\t<\/div><\/div><\/div><div 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ow-button-align-center\">\n\t<a\n\thref=\"http:\/\/www.asimas.it\/new_asimas\/la-diagnosi\/\"\n\t\tclass=\"ow-icon-placement-left ow-button-hover\" \t>\n\t\t<span>\n\t\t\t\n\t\t\tDiagnosi\t\t<\/span>\n\t<\/a>\n<\/div>\n<\/div><\/div><\/div><div id=\"panel-47-1-0-2\" class=\"so-panel widget widget_sow-button panel-last-child\" data-index=\"3\" ><div\n\t\t\t\n\t\t\tclass=\"so-widget-sow-button so-widget-sow-button-atom-c82ac91d79c0-47\"\n\t\t\t\n\t\t><div class=\"ow-button-base ow-button-align-center\">\n\t<a\n\thref=\"https:\/\/associazionerima.it\/\"\n\t\tclass=\"ow-icon-placement-left ow-button-hover\" target=\"_blank\" rel=\"noopener noreferrer\" \t>\n\t\t<span>\n\t\t\t\n\t\t\tRima\t\t<\/span>\n\t<\/a>\n<\/div>\n<\/div><\/div><\/div><div id=\"pgc-47-1-1\"  class=\"panel-grid-cell\" ><div id=\"panel-47-1-1-0\" class=\"so-panel widget widget_sow-button panel-first-child\" data-index=\"4\" ><div class=\"panel-widget-style panel-widget-style-for-47-1-1-0\" ><div\n\t\t\t\n\t\t\tclass=\"so-widget-sow-button so-widget-sow-button-flat-59efebd230a8-47\"\n\t\t\t\n\t\t><div class=\"ow-button-base ow-button-align-center\">\n\t<a\n\thref=\"http:\/\/www.asimas.it\/new_asimas\/noi-malati\/\"\n\t\tclass=\"ow-icon-placement-left ow-button-hover\" \t>\n\t\t<span>\n\t\t\t\n\t\t\tNoi malati\t\t<\/span>\n\t<\/a>\n<\/div>\n<\/div><\/div><\/div><div id=\"panel-47-1-1-1\" class=\"so-panel widget widget_sow-button\" data-index=\"5\" ><div class=\"panel-widget-style panel-widget-style-for-47-1-1-1\" ><div\n\t\t\t\n\t\t\tclass=\"so-widget-sow-button so-widget-sow-button-flat-59efebd230a8-47\"\n\t\t\t\n\t\t><div class=\"ow-button-base ow-button-align-center\">\n\t<a\n\thref=\"http:\/\/www.asimas.it\/new_asimas\/la-triptasi\/\"\n\t\tclass=\"ow-icon-placement-left ow-button-hover\" \t>\n\t\t<span>\n\t\t\t\n\t\t\tTriptasi\t\t<\/span>\n\t<\/a>\n<\/div>\n<\/div><\/div><\/div><div id=\"panel-47-1-1-2\" class=\"so-panel widget widget_sow-button panel-last-child\" data-index=\"6\" ><div class=\"panel-widget-style panel-widget-style-for-47-1-1-2\" ><div\n\t\t\t\n\t\t\tclass=\"so-widget-sow-button so-widget-sow-button-flat-59efebd230a8-47\"\n\t\t\t\n\t\t><div class=\"ow-button-base ow-button-align-center\">\n\t<a\n\thref=\"http:\/\/www.asimas.it\/new_asimas\/ambulatori\/\"\n\t\tclass=\"ow-icon-placement-left ow-button-hover\" \t>\n\t\t<span>\n\t\t\t\n\t\t\tAmbulatori\t\t<\/span>\n\t<\/a>\n<\/div>\n<\/div><\/div><\/div><\/div><div id=\"pgc-47-1-2\"  class=\"panel-grid-cell\" ><div id=\"panel-47-1-2-0\" class=\"so-panel widget widget_sow-button panel-first-child\" data-index=\"7\" ><div class=\"panel-widget-style panel-widget-style-for-47-1-2-0\" ><div\n\t\t\t\n\t\t\tclass=\"so-widget-sow-button so-widget-sow-button-flat-59efebd230a8-47\"\n\t\t\t\n\t\t><div class=\"ow-button-base ow-button-align-center\">\n\t<a\n\thref=\"http:\/\/www.asimas.it\/new_asimas\/sezione-pediatrica\/\"\n\t\tclass=\"ow-icon-placement-left ow-button-hover\" \t>\n\t\t<span>\n\t\t\t\n\t\t\tPediatria\t\t<\/span>\n\t<\/a>\n<\/div>\n<\/div><\/div><\/div><div id=\"panel-47-1-2-1\" class=\"so-panel widget widget_sow-button\" data-index=\"8\" ><div class=\"panel-widget-style panel-widget-style-for-47-1-2-1\" ><div\n\t\t\t\n\t\t\tclass=\"so-widget-sow-button so-widget-sow-button-flat-59efebd230a8-47\"\n\t\t\t\n\t\t><div class=\"ow-button-base ow-button-align-center\">\n\t<a\n\thref=\"http:\/\/www.asimas.it\/new_asimas\/consigli\/\"\n\t\tclass=\"ow-icon-placement-left ow-button-hover\" \t>\n\t\t<span>\n\t\t\t\n\t\t\tConsigli\t\t<\/span>\n\t<\/a>\n<\/div>\n<\/div><\/div><\/div><div id=\"panel-47-1-2-2\" class=\"so-panel widget widget_sow-button panel-last-child\" data-index=\"9\" ><div class=\"panel-widget-style panel-widget-style-for-47-1-2-2\" ><div\n\t\t\t\n\t\t\tclass=\"so-widget-sow-button so-widget-sow-button-flat-59efebd230a8-47\"\n\t\t\t\n\t\t><div class=\"ow-button-base ow-button-align-center\">\n\t<a\n\thref=\"http:\/\/www.asimas.it\/new_asimas\/malattie-rare\/\"\n\t\tclass=\"ow-icon-placement-left ow-button-hover\" \t>\n\t\t<span>\n\t\t\t\n\t\t\tMalattie rare\t\t<\/span>\n\t<\/a>\n<\/div>\n<\/div><\/div><\/div><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>La mastocitosi \u00e8 una patologia rara, che include un gruppo di disordini estremamente eterogenei per sintomatologia, decorso clinico e prognosi, caratterizzati da proliferazione ed accumulo di mastociti patologici in differenti [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"full-width.php","meta":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v18.4.1 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\r\n<title>Cos&#039;\u00e8 la Mastocitosi? | ASIMAS | Associazione Italiana Mastocitosi<\/title>\r\n<meta name=\"description\" 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